Aim: Prader-Willi syndrome (PWS) is a genetic disorder historically characterized by two phenotypic stages. The early phenotype in infants is associated with hypotonia, poor suck, and failure to thrive. In later childhood, PWS is associated with intellectual disability, hyperphagia, as well as growth and sex hormone deficiency. Little is known…

Background: Behaviour problems and a preference for adult contact are reported to be prominent in the phenotype of Smith-Magenis syndrome. In this study we examined the relationship between social interactions and self-injurious and aggressive/disruptive behaviour in Smith-Magenis syndrome to explore potential operant reinforcement of problem…

Autism spectrum disorders (ASDs) are more frequently associated with tic disorders than expected by chance. Variable rates of comorbidity have been reported and common genetic and neurobiological factors are probably involved. The aim of this study was to determine the rate of tic disorders in a clinical sample (n = 105) of children and…

Mentally retarded emotionally disturbed children (N=31) were compared on the Child Depression Inventory and the Child Behavior Profile with 31 children in a normal school setting. Correlational data showed a strong relationship between the cut-off scores for both measures suggesting that similarities exist between depression in mentally retarded…

Twenty-nine educable mentally retarded children (9-12 years old) were observed while they worked on academic and nonacademic tasks to investigate the hypothesis that retarded children are more distractible and/or more out directed than nonretarded children. (Author/CL)

In this response to critiques (Mudford, Hogg and Roberts 1997, 1999) of the use of behavior states in research involving individuals with mental retardation, it is argued that the work on behavioral state analysis by Robert D. Guess has contributed to the field at the practical, empirical, and theoretical levels. (Contains references.) (CR)

Caregivers of 55 boys with fragile X syndrome (ages 3-12) and 57 matched controls completed five behavioral questionnaires. Principal components analysis yielded 5 behavioral clusters: abnormal language, tactile defensiveness, poor self-control, poor eye contact/shyness, and hand flapping. Boys with fragile X were four times more likely to have…

Three experiments were conducted with two participants with mental retardation that displayed property destruction and stereotypy. The experiments assessed the function of the responses, determined their relationship, and developed a treatment to reduce property destruction. Response blocking reduced property destruction (and attempts), prevented…

A study attempted to replicate a previous study that presented reliability data from recordings of behavior state using a 13-category coding system. Replication was unsuccessful. Obtained mean percentage agreement on occurrence for individual behavior state and participants (n=34) ranged across observer pairs from 0 to 58 percent. (Contains 13…

The classroom behaviors of 12 segregated and 14 integrated educable mentally retarded (EMR) children (mean age 10 years) who were all formerly segregated and then randomly assigned to their present class placement were compared to those of a low IQ group who had never been identified for special class placements and an intellectually average group…

Assessed was the degree to which classification of mental retardation levels based upon a measure of adaptive behavior (the Vineland Social Maturity Scale) differed from the classification based upon IQ for Negro and Caucasian children, 4 to 17 years of age. (Author)

Results of a questionnaire indicate that most parents feel their children had no problems dealing with sex, although very few children had received sex information either in school or at home. A need is suggested for more comprehensive research in this area. (CJ)

The characteristics of a group of 17 mentally retarded institutionalized individuals (ages 6 to 51) with self-injurious behavior (SIB) were compared with those of 14 patients without SIB. Among findings were that 65 percent of the SIB group were females, that the SIB group had an elevated pulse rate, and that they slept less. (PHR)

A study of 22 children with autism and 19 children with mental retardation found that, when prompted, school-age and adolescent subjects with autism did not differ from children with mental retardation in production of functional play acts and situationally appropriate object substitution, but did produce fewer novel pretend play acts. (CR)