The association of hearing loss and retinitis pigmentosa has been generally recognized as the genetic disorder of Usher's syndrome. The article reviews findings of this syndrome and suggests strategies for dealing with the clinical and psychological problems displayed by Usher's syndrome patients. (Author/SW)

Group counseling for secondary students with Usher's syndrome, a genetic condition resulting in hearing impairment at birth and gradual loss of vision, was intended to provide information and opportunities for expression. Results included practical changes in school environment, increased information about deaf-blindness for the students, and help…

This article describes a model sex education program developed for youths and adults who are deafblind by the Helen Keller National Center for Deaf-Blind Youths and Adults. In addition, it also discusses major related issues and presents general recommendations and a resource for further information. (Contains 11 references.) (Author/CR)

Usher's syndrome, a genetic condition causing congenital profound hearing loss and a progressive blindness due to retinitis pigmentosa, affects an estimated three to six percent of children in educational and rehabilitative programs for the hearing impaired. (Author)

Three major limiting factors are outlined: the lack of appropriate psychological tests, the dearth of properly trained psychologists, and the failure to obtain complete case histories. Several methods of overcoming these drawbacks are described. (Author/DLS)

A rationale and practical guide to the psychological evaluation of deaf-blind children is provided. Few adequate tests exist. The Callier Azusa Scale, designed specifically for this population, is recommended as the best instrument. Some items on the Learning Accomplishment Profile are appropriate. Operationally stated skill checklists are also…