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Pinheiro, Ana P.; Galdo-Alvarez, Santiago; Rauber, Andreia; Sampaio, Adriana; Niznikiewicz, Margaret; Goncalves, Oscar F. – Research in Developmental Disabilities: A Multidisciplinary Journal, 2011
Williams syndrome (WS), a neurodevelopmental genetic disorder due to a microdeletion in chromosome 7, is described as displaying an intriguing socio-cognitive phenotype. Deficits in prosody production and comprehension have been consistently reported in behavioral studies. It remains, however, to be clarified the neurobiological processes…
Descriptors: Genetic Disorders, Sentences, Age, Semantics
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Pinheiro, Ana P.; Galdo-Alvarez, Santaigo; Sampaio, Adriana; Niznikiewicz, Margaret; Goncalves, Oscar F. – Research in Developmental Disabilities: A Multidisciplinary Journal, 2010
Williams syndrome (WS), a genetic neurodevelopmental disorder due to microdeletion in chromosome 7, has been described as a syndrome with an intriguing socio-cognitive phenotype. Cognitively, the relative preservation of language and face processing abilities coexists with severe deficits in visual-spatial tasks, as well as in tasks involving…
Descriptors: Sentences, Semantics, Language Processing, Spatial Ability